Volumen 20 números 1 y 2 - 2023
ISSN 0718-0918
Tabla de Contenidos > Caso Clínico
Natalia Peñaloza Barrios1, Marcela Osorio Santos2 Sharon Romero Vergara3, María Camila Arévalo Pérez1, Carolina María Díaz Guerra1, Heidy María Marsiglia Armella1 2, Andrea Carolina Zárate Vergara4, Irina Suley Tirado Pérez5
1 Servicio de Hemato Oncología Pediátrica, Hospital Infantil Napoleón Franco Pareja (CTG, CO)
2 Especialización en Pediatría, Facultad de Medicina, Universidad de Cartagena (CTG, CO)
3 Especialización en Pediatría, Facultad de Ciencias de la Salud, Universidad de Libre (BAQ, CO)
4 Especialista en cuidado intensivo pediátrico, Clínica especializada la Concepción (SJO, CO)
5 Médica epidemióloga, Máster cuidado paliativo pediátrico, Especialización en Pediatría, Facultad de Ciencias de la Salud, Corporación Universitaria Remington (CUR), (MED, CO)

Resumen | Abstract | Texto completo HTML | Descargar cuerpo en pdf

Introduction: Primary malignant tumors of the liver are extremely rare. It represents only 1% of all malignancies in the pediatric age group, with less than 1.5 cases per million children under 18 years of age. Hepatoblastoma is the most common primary hepatic neoplasm (48%); Hepatocellular carcinoma is the second most common primary liver neoplasm in childhood (27%), and the rest are vascular tumors and sarcomas. The type of fibrolamellar hepatocellular carcinoma is rare, usually seen in the older age group (median age 26 ,4 years).

Clinical case: The case report is made since there are few cases reported in the literature, it is an 11-year-old patient who suffers trauma to the abdomen due to a fall on a bicycle, which is why she consults, draws attention with no previous history, totally asymptomatic, but with increased hepatomegaly and abdominal pain during hospitalization, for which extension studies were performed, with evidence by contrast magnetic resonance, of a tumor lesion that involved the entire right hepatic lobe with confirmation by biopsy of a fibrolamellar variant.

Conclusion: Liver tumors are infrequent, the fibrolamellar variant is even more unusual, the typical age of presentation is young adults, for which its presentation in pediatric age is very scarce; Initially, its management is based on surgical resection, depending on the stage presented at the time of diagnosis.

Key words: Fibrolamellar hepatocellular carcinoma, hepatocellular carcinoma, carcinoma, hepatic neoplasia, pediatric

Revista Pediatría Electrónica
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ISSN 0718-0918