Introduction
Ewing's sarcoma is the second most common bone tumor of childhood and adolescence, although it can also occur in soft tissues. It is an aggressive neoplasm with improved survival thanks to medical advances, reaching survival in 70% of cases; however, an atypical presentation is related to a poor prognosis.
Objective
To carry out a case report with an atypical presentation in an adolescent with clinical and radiological characteristics of rapid-onset skeletal metastases (within 4 weeks after diagnosis) and to review the current literature on this pathology.
Clinical case
This is a case of a 14-year-old adolescent with no significant pathological history with Ewing's sarcoma, who debuted with a rapidly evolving lesion in the frontal area, being an atypical presentation, which is related to decreased survival.
Conclusions
Ewing's sarcoma is an aggressive malignant neoplasm that mainly affects the skeletal system in children and young adults; there are several factors related to the management and prognosis of these patients. An unusual presentation is associated with a poor prognosis.
Keywords: Sarcoma, Ewing, Extraosseous Ewing sarcoma, Adolescent |