Volumen 15 número 3 - Octubre 2018 |
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ISSN 0718-0918 |
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Tabla de Contenidos > Caso Clínico |
SÍNDROME DE KASABACH- MERRIT
Nelson Armando muñoz1, Soraya Cristina Paternina Palomo2, Lissette Lorena Guevara Flórez3, Irina Suley Tirado Pérez4, Andrea Carolina Zárate Vergara5, Ángel Castro Dájer6
1 Médico Pediatra, Universidad de Cartagena – Hospital Infantil Napoleón Franco Pareja
2 Médico Pediatra Hematooncologo, Universidad de Cartagena – Hospital Infantil Napoleón Franco Pareja
3 Médico pediatra, Universidad de Cartagena
4 Médico Epidemiólogo, Master en cuidados paliativos pediátrico, residente de cuidados intensivos pediátrico, Universidad de Santander
5 Medico Epidemiólogo, residente de cuidados intensivos pediátrico, Universidad de Santander
6 Médico Pediatra Hematooncologo – Clínica Blas de Lezo
Resumen |Abstract | Texto completo | Descargar cuerpo en pdf |
Introduction: The Kasabach-Merritt syndrome (SKM) is rare, has a high mortality and is characterized by a vascular lesion of rapid growth, associated with coagulopathy of consumption and thrombocytopenia.
Materials and methods: review of current literature in comparison with articles of reviews of subjects in electronic search in databases of RIMA, MEDLINE, PUB-MED, MEDSCAPE, from 1940 to 2017.
Results A clinical case of a 10-month-old child is described. of age with Kasabach Merrit syndrome occurred at the Napoleon Franco Franco Children's Hospital (HINFP)
Conclusions The Kasabach-Merritt syndrome is a rare entity, its diagnosis starts from the clinical suspicion, which includes the physical examination the finding of a hemangioma accompanied by thrombocytopenia and coagulopathy. The management is not scheduled, corticoid is available as start therapy, interferon, antineoplastic, radiotherapy or surgery, and its prognosis will depend on the prompt resolution. |
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